Fahr Disease

Fahr disease: Idiopathic basal ganglia calcification

Transcranial sonography of basal ganglia calcifications in Fahr disease.

Fahr disease, also known as bilateral striopallidodentate calcinosis, is a rare degenerative neurologic disorder characterized by almost symmetric calcifications of the basal ganglia, the cerebellum dentate nuclei, the thalami, and the white matter of the cerebral hemispheres. Bilateral striopallidodentate calcinosis manifests as familial autosomal dominant but also as sporadic forms. Movement ...

fahr disease: idiopathic basal ganglia calcification

-

Fahr Syndrome Unknown Complication: Overactive Bladder

A 38-year-old male patient was admitted to our outpatient department because of frequency and urgency incontinence. During evaluation it was detected that the patient was suffering from frequency which was progressive for one year, feeling of incontinence, and urgency incontinence. There was no urologic pathology detected in patient's medical and family history. Neurologic consultation was requ...

Teaching NeuroImages: Fahr syndrome caused by hypoparathyroidism.

A57-year-old woman with a remote history of thyroidectomy but no prior neurologic symptoms developed seizures, fever, and coma. Limited evaluation at her local hospital in rural Haiti demonstrated serum hypocalcemia (4 mg/dL) and extensive bilateral subcortical calcification in the cerebral and cerebellar hemispheres on CT (figure). This pattern of calcification can occur in inherited condition...